Title |
Desmoid-type fibromatosis of the head and neck in children: a case report and review of the literature
|
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Published in |
Journal of Medical Case Reports, June 2016
|
DOI | 10.1186/s13256-016-0949-9 |
Pubmed ID | |
Authors |
Hidetaka Miyashita, Seiji Asoda, Tomoya Soma, Kanako Munakata, Masaki Yazawa, Taneaki Nakagawa, Hiromasa Kawana |
Abstract |
Desmoid-type fibromatosis is defined as an intermediate tumor that rarely occurs in the head and neck of children. There is no doubt as to the value of complete surgical excision for desmoid-type fibromatosis. However, in pediatric patients, surgeons may often be concerned about making a wide excision because of the potential for functional morbidity. Some studies have reported a lack of correlation between margin status and recurrence. Therefore, we discussed our findings with a focus on the state of surgical margins. We report an unusual case of a 9-month-old Japanese girl who prior to presenting at our hospital underwent debulking surgery twice with chemotherapy for desmoid-type fibromatosis of the tongue at another hospital. We performed a partial glossectomy and simultaneous reconstruction with local flap and achieved microscopic complete resection. We also reviewed available literature of pediatric desmoid-type fibromatosis in the head and neck. We described successful treatment for the refractory case of pediatric desmoid-type fibromatosis. The review results showed that some microscopic incomplete resections of tumors in pediatric patients with desmoid-type fibromatosis tended to be acceptable with surgical treatment. |
X Demographics
Geographical breakdown
Country | Count | As % |
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Venezuela, Bolivarian Republic of | 1 | 100% |
Demographic breakdown
Type | Count | As % |
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Science communicators (journalists, bloggers, editors) | 1 | 100% |
Mendeley readers
Geographical breakdown
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Unknown | 29 | 100% |
Demographic breakdown
Readers by professional status | Count | As % |
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Student > Doctoral Student | 7 | 24% |
Other | 5 | 17% |
Student > Master | 3 | 10% |
Student > Bachelor | 2 | 7% |
Lecturer | 1 | 3% |
Other | 3 | 10% |
Unknown | 8 | 28% |
Readers by discipline | Count | As % |
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Medicine and Dentistry | 16 | 55% |
Unspecified | 1 | 3% |
Neuroscience | 1 | 3% |
Pharmacology, Toxicology and Pharmaceutical Science | 1 | 3% |
Unknown | 10 | 34% |