Title |
Regional consensus opinion for the management of Beta thalassemia major in the Arabian Gulf area
|
---|---|
Published in |
Orphanet Journal of Rare Diseases, September 2013
|
DOI | 10.1186/1750-1172-8-143 |
Pubmed ID | |
Authors |
Mohamad H Qari, Yasser Wali, Muneer H Albagshi, Mohammad Alshahrani, Azzah Alzahrani, Ibrahim A Alhijji, Abdulkareem Almomen, Abdullah Aljefri, Hussain H Al Saeed, Shaker Abdullah, Ahmad Al Rustumani, Khoutir Mahour, Shaker A Mousa |
Abstract |
Thalassemia syndrome has diverse clinical presentations and a global spread that has far exceeded the classical Mediterranean basin where the mutations arose. The mutations that give rise to either alpha or beta thalassemia are numerous, resulting in a wide spectrum of clinical severity ranging from carrier state to life-threatening, inherited hemolytic anemia that requires regular blood transfusion. Beta thalassemia major constitutes a remarkable challenge to health care providers. The complications arising due to the anemia, transfusional iron overload, as well as other therapy-related complications add to the complexity of this condition. To produce this consensus opinion manuscript, a PubMed search was performed to gather evidence-based original articles, review articles, as well as published work reflecting the experience of physicians and scientists in the Arabian Gulf region in an effort to standardize the management protocol. |
X Demographics
Geographical breakdown
Country | Count | As % |
---|---|---|
United States | 1 | 50% |
Unknown | 1 | 50% |
Demographic breakdown
Type | Count | As % |
---|---|---|
Members of the public | 1 | 50% |
Scientists | 1 | 50% |
Mendeley readers
Geographical breakdown
Country | Count | As % |
---|---|---|
Indonesia | 1 | <1% |
Unknown | 109 | 99% |
Demographic breakdown
Readers by professional status | Count | As % |
---|---|---|
Student > Bachelor | 13 | 12% |
Student > Master | 11 | 10% |
Researcher | 10 | 9% |
Student > Ph. D. Student | 10 | 9% |
Other | 5 | 5% |
Other | 17 | 15% |
Unknown | 44 | 40% |
Readers by discipline | Count | As % |
---|---|---|
Medicine and Dentistry | 35 | 32% |
Biochemistry, Genetics and Molecular Biology | 8 | 7% |
Nursing and Health Professions | 6 | 5% |
Agricultural and Biological Sciences | 6 | 5% |
Immunology and Microbiology | 2 | 2% |
Other | 8 | 7% |
Unknown | 45 | 41% |