Title |
FGF10 Signaling differences between type I pleuropulmonary blastoma and congenital cystic adenomatoid malformation
|
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Published in |
Orphanet Journal of Rare Diseases, September 2013
|
DOI | 10.1186/1750-1172-8-130 |
Pubmed ID | |
Authors |
Guillaume Lezmi, Virginie Verkarre, Naziha Khen-Dunlop, Shamila Vibhushan, Alice Hadchouel, Caroline Rambaud, Marie-Christine Copin, Jean-Luc Rittie, Alexandra Benachi, Jean-Christophe Fournet, Christophe Delacourt |
Abstract |
Type I pleuropulmonary blastoma (PPB) and congenital cystic adenomatoid malformation of the lung (CCAM) are cystic lung diseases of childhood. Their clinical and radiological presentations are often similar, and pathologic discrimination remains difficult in many cases. As a consequence, type I PPB and CCAM are frequently confused, leading to delayed adequate management for type I PPB. Recent studies have suggested a role for fibroblast growth factor (FGF) 10 signal pathway in CCAM pathogenesis. The objective of our study was to determine whether FGF10 signaling differs between CCAM and type I PPB. |
Mendeley readers
Geographical breakdown
Country | Count | As % |
---|---|---|
Nigeria | 1 | 3% |
Unknown | 31 | 97% |
Demographic breakdown
Readers by professional status | Count | As % |
---|---|---|
Researcher | 6 | 19% |
Student > Ph. D. Student | 4 | 13% |
Student > Postgraduate | 3 | 9% |
Student > Bachelor | 3 | 9% |
Student > Doctoral Student | 2 | 6% |
Other | 7 | 22% |
Unknown | 7 | 22% |
Readers by discipline | Count | As % |
---|---|---|
Medicine and Dentistry | 14 | 44% |
Agricultural and Biological Sciences | 4 | 13% |
Nursing and Health Professions | 2 | 6% |
Biochemistry, Genetics and Molecular Biology | 2 | 6% |
Psychology | 1 | 3% |
Other | 1 | 3% |
Unknown | 8 | 25% |