Title |
Encephalopathic Susac’s Syndrome associated with livedo racemosa in a young woman before the completion of family planning
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Published in |
BMC Neurology, November 2013
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DOI | 10.1186/1471-2377-13-185 |
Pubmed ID | |
Authors |
Maik Engeholm, Beate Leo-Kottler, Hansjörg Rempp, Tobias Lindig, Holger Lerche, Ilka Kleffner, Melanie Henes, Marcel Dihné |
Abstract |
Susac's Syndrome (SS) consists of the triad of encephalopathy, branch retinal artery occlusions (BRAO) and hearing loss (HL). Histopathologically, SS is characterised by a microangiopathy, and some observations suggest that an immune-mediated damage of endothelial cells might play a role. These findings also implicate a similarity between SS and other autoimmune diseases, most notably juvenile dermatomyositis (JDM). However, SS and JDM are commonly thought to affect distinct and non-overlapping sets of organs, and it is currently not clear how these specificities arise. Moreover, in the absence of clinical trials, some authors suggest that therapeutic approaches in SS should rely on the model of other autoimmune diseases such as JDM. |
X Demographics
Geographical breakdown
Country | Count | As % |
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Germany | 1 | 33% |
Egypt | 1 | 33% |
Unknown | 1 | 33% |
Demographic breakdown
Type | Count | As % |
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Members of the public | 2 | 67% |
Practitioners (doctors, other healthcare professionals) | 1 | 33% |
Mendeley readers
Geographical breakdown
Country | Count | As % |
---|---|---|
Unknown | 77 | 100% |
Demographic breakdown
Readers by professional status | Count | As % |
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Student > Master | 16 | 21% |
Student > Ph. D. Student | 15 | 19% |
Student > Bachelor | 6 | 8% |
Researcher | 5 | 6% |
Student > Doctoral Student | 4 | 5% |
Other | 7 | 9% |
Unknown | 24 | 31% |
Readers by discipline | Count | As % |
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Medicine and Dentistry | 27 | 35% |
Psychology | 7 | 9% |
Neuroscience | 4 | 5% |
Business, Management and Accounting | 3 | 4% |
Nursing and Health Professions | 3 | 4% |
Other | 9 | 12% |
Unknown | 24 | 31% |