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IgG4- related disease: an orphan disease with many faces

Overview of attention for article published in Orphanet Journal of Rare Diseases, July 2014
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  • In the top 25% of all research outputs scored by Altmetric
  • High Attention Score compared to outputs of the same age (92nd percentile)
  • High Attention Score compared to outputs of the same age and source (93rd percentile)

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28 X users
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1 Facebook page
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1 Wikipedia page

Citations

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79 Dimensions

Readers on

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140 Mendeley
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Title
IgG4- related disease: an orphan disease with many faces
Published in
Orphanet Journal of Rare Diseases, July 2014
DOI 10.1186/s13023-014-0110-z
Pubmed ID
Authors

Herwig Pieringer, Ilse Parzer, Adelheid Wöhrer, Petra Reis, Bastian Oppl, Jochen Zwerina

Abstract

Immunoglobulin G4- related disease (IgG4-RD) is a rare systemic fibro-inflammatory disorder (ORPHA284264). Although patients have been described more than 100 years ago, the systemic nature of this disease has been recognized in the 21st century only. Type 1 autoimmune pancreatitis is the most frequent manifestation of IgG4-RD. However, IgG4-RD can affect any organ such as salivary glands, orbits, retroperitoneum and many others. Recent research enabled a clear clinical and histopathological description of IgG4-RD. Typically, lymphoplasmacellular inflammation, storiform fibrosis and obliterative phlebitis are found in IgG4-RD biopsies and the tissue invading plasma cells largely produce IgG4. Elevated serum IgG4 levels are found in many but not all patients. Consequently, diagnostic criteria for IgG4-RD have been proposed recently. Treatment is largely based on clinical experience and retrospective case series. Glucocorticoids are the mainstay of therapy, although adjunctive immunosuppressive agents are used in relapsing patients. This review summarizes current knowledge on clinical manifestations, pathophysiology and treatment of IgG4-RD.

X Demographics

X Demographics

The data shown below were collected from the profiles of 28 X users who shared this research output. Click here to find out more about how the information was compiled.
Mendeley readers

Mendeley readers

The data shown below were compiled from readership statistics for 140 Mendeley readers of this research output. Click here to see the associated Mendeley record.

Geographical breakdown

Country Count As %
United States 1 <1%
Portugal 1 <1%
South Africa 1 <1%
Unknown 137 98%

Demographic breakdown

Readers by professional status Count As %
Other 23 16%
Student > Doctoral Student 16 11%
Researcher 14 10%
Student > Master 14 10%
Student > Ph. D. Student 13 9%
Other 41 29%
Unknown 19 14%
Readers by discipline Count As %
Medicine and Dentistry 80 57%
Agricultural and Biological Sciences 9 6%
Immunology and Microbiology 6 4%
Nursing and Health Professions 6 4%
Biochemistry, Genetics and Molecular Biology 5 4%
Other 9 6%
Unknown 25 18%
Attention Score in Context

Attention Score in Context

This research output has an Altmetric Attention Score of 19. This is our high-level measure of the quality and quantity of online attention that it has received. This Attention Score, as well as the ranking and number of research outputs shown below, was calculated when the research output was last mentioned on 06 February 2024.
All research outputs
#1,911,283
of 25,563,770 outputs
Outputs from Orphanet Journal of Rare Diseases
#211
of 3,150 outputs
Outputs of similar age
#18,617
of 242,109 outputs
Outputs of similar age from Orphanet Journal of Rare Diseases
#4
of 46 outputs
Altmetric has tracked 25,563,770 research outputs across all sources so far. Compared to these this one has done particularly well and is in the 92nd percentile: it's in the top 10% of all research outputs ever tracked by Altmetric.
So far Altmetric has tracked 3,150 research outputs from this source. They typically receive more attention than average, with a mean Attention Score of 8.2. This one has done particularly well, scoring higher than 93% of its peers.
Older research outputs will score higher simply because they've had more time to accumulate mentions. To account for age we can compare this Altmetric Attention Score to the 242,109 tracked outputs that were published within six weeks on either side of this one in any source. This one has done particularly well, scoring higher than 92% of its contemporaries.
We're also able to compare this research output to 46 others from the same source and published within six weeks on either side of this one. This one has done particularly well, scoring higher than 93% of its contemporaries.