Title |
A case of lethal spontaneous massive hemothorax in a patient with neurofibromatosis 1
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Published in |
Journal of Cardiothoracic Surgery, October 2014
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DOI | 10.1186/s13019-014-0172-y |
Pubmed ID | |
Authors |
Luisa Zacarias Föhrding, Timur Sellmann, Sebastian Angenendt, Detlef Kindgen-Milles, Stefan A Topp, Bernhard Korbmacher, Artur Lichtenberg, Wolfram T Knoefel |
Abstract |
Neurofibromatosis type 1 is an autosomal dominant disease characterized by multiple dermatological disorders amongst others. Among the less frequent manifestations are vascular abnormalities. Here, we present a case of spontaneous massive hemothorax in a 39-year-old Caucasian woman with neurofibromatosis 1 and a thoracic meningocele with a lethal outcome despite extensive surgical intervention as well as intensive care measures. Spontaneous hemothorax is a rare, but potentially lethal complication of neurofibromatosis type 1, which necessitates quick and decisive intervention; endovascular embolization where possible, otherwise aggressive surgical intervention in unstable patients. |
Mendeley readers
Geographical breakdown
Country | Count | As % |
---|---|---|
Unknown | 7 | 100% |
Demographic breakdown
Readers by professional status | Count | As % |
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Student > Doctoral Student | 2 | 29% |
Professor | 1 | 14% |
Student > Ph. D. Student | 1 | 14% |
Student > Master | 1 | 14% |
Researcher | 1 | 14% |
Other | 1 | 14% |
Readers by discipline | Count | As % |
---|---|---|
Medicine and Dentistry | 6 | 86% |
Nursing and Health Professions | 1 | 14% |