Title |
Extraordinary disease-free survival in a rare malignant extrarenal rhabdoid tumor: a case report and review of the literature
|
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Published in |
Journal of Medical Case Reports, February 2018
|
DOI | 10.1186/s13256-017-1554-2 |
Pubmed ID | |
Authors |
Francesco D’Amico, Alessandra Bertacco, Maurizio Cesari, Claudia Mescoli, Giorgio Caturegli, Gabriel Gondolesi, Umberto Cillo |
Abstract |
Malignant extrarenal rhabdoid tumor of the gastrointestinal tract is rarely reported in the literature. It is characterized by poor prognosis and aggressive metastatic features. A literature review evidenced only 19 cases, with poor outcome. We report a case of a colonic "pure" malignant extrarenal rhabdoid tumor with metastatic nodes in a 65-year-old Caucasian man. He was treated surgically with no recurrence, no adjuvant chemotherapy, and with 4-year survival without disease at the time of the submission of this article. We present an extraordinary case of long-term survival due to the extended surgical treatment. We believe that the absence of organ metastasis at presentation is a positive prognostic factor, although pathology confirmed node involvement (13/38 positive) on microscopy. |
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Geographical breakdown
Country | Count | As % |
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United Kingdom | 1 | 100% |
Demographic breakdown
Type | Count | As % |
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Scientists | 1 | 100% |
Mendeley readers
Geographical breakdown
Country | Count | As % |
---|---|---|
Unknown | 24 | 100% |
Demographic breakdown
Readers by professional status | Count | As % |
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Student > Ph. D. Student | 4 | 17% |
Other | 3 | 13% |
Student > Doctoral Student | 2 | 8% |
Researcher | 2 | 8% |
Professor | 1 | 4% |
Other | 3 | 13% |
Unknown | 9 | 38% |
Readers by discipline | Count | As % |
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Medicine and Dentistry | 10 | 42% |
Nursing and Health Professions | 3 | 13% |
Agricultural and Biological Sciences | 1 | 4% |
Unknown | 10 | 42% |