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Cerebellar cognitive affective syndrome: insights from Joubert syndrome

Overview of attention for article published in Cerebellum & Ataxias, March 2018
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About this Attention Score

  • Above-average Attention Score compared to outputs of the same age (62nd percentile)

Mentioned by

6 tweeters
1 Facebook page


16 Dimensions

Readers on

40 Mendeley
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Cerebellar cognitive affective syndrome: insights from Joubert syndrome
Published in
Cerebellum & Ataxias, March 2018
DOI 10.1186/s40673-018-0085-y
Pubmed ID

Chelsea L. Hickey, Janet C. Sherman, Paula Goldenberg, Amy Kritzer, Paul Caruso, Jeremy D. Schmahmann, Mary K. Colvin


Joubert syndrome (JS) is a rare, autosomal recessively inherited genetic disorder characterized morphologically by unique developmental malformations of the cerebellum and brainstem (the molar tooth sign), and clinically by impaired motor functions and intellectual disability. Patients with JS often face multiple cognitive challenges, but the neuropsychological profile of this condition has not been well characterized. We performed comprehensive neurological and neuropsychological evaluations in three adult brothers with JS, ages 32, 27, and 25 years. They all exhibited impaired motor control, global developmental delay most evident in executive function, affect regulation, and social skill set, and similar patterns of neuropsychiatric symptoms. These findings provide new insights into the intellectual and neurobehavioral phenotype of JS, which we regard as a developmental form of the cerebellar cognitive affective / Schmahmann syndrome (CCAS). These observations have direct clinical relevance for the diagnosis and care of patients with JS, and they help further the understanding of the multiple manifestations of atypical cerebrocerebellar development.

Twitter Demographics

The data shown below were collected from the profiles of 6 tweeters who shared this research output. Click here to find out more about how the information was compiled.

Mendeley readers

The data shown below were compiled from readership statistics for 40 Mendeley readers of this research output. Click here to see the associated Mendeley record.

Geographical breakdown

Country Count As %
Unknown 40 100%

Demographic breakdown

Readers by professional status Count As %
Researcher 6 15%
Student > Ph. D. Student 6 15%
Student > Bachelor 4 10%
Student > Postgraduate 4 10%
Student > Master 4 10%
Other 5 13%
Unknown 11 28%
Readers by discipline Count As %
Neuroscience 5 13%
Psychology 4 10%
Nursing and Health Professions 4 10%
Medicine and Dentistry 4 10%
Biochemistry, Genetics and Molecular Biology 3 8%
Other 6 15%
Unknown 14 35%

Attention Score in Context

This research output has an Altmetric Attention Score of 4. This is our high-level measure of the quality and quantity of online attention that it has received. This Attention Score, as well as the ranking and number of research outputs shown below, was calculated when the research output was last mentioned on 24 July 2018.
All research outputs
of 17,131,911 outputs
Outputs from Cerebellum & Ataxias
of 96 outputs
Outputs of similar age
of 287,377 outputs
Outputs of similar age from Cerebellum & Ataxias
of 1 outputs
Altmetric has tracked 17,131,911 research outputs across all sources so far. This one has received more attention than most of these and is in the 69th percentile.
So far Altmetric has tracked 96 research outputs from this source. They receive a mean Attention Score of 3.0. This one has done well, scoring higher than 77% of its peers.
Older research outputs will score higher simply because they've had more time to accumulate mentions. To account for age we can compare this Altmetric Attention Score to the 287,377 tracked outputs that were published within six weeks on either side of this one in any source. This one has gotten more attention than average, scoring higher than 62% of its contemporaries.
We're also able to compare this research output to 1 others from the same source and published within six weeks on either side of this one. This one has scored higher than all of them